Although access to this page is not restricted, the information found here is intended for use by medical providers. A report of 140 cases with special regard to the development of secondary malignant tumors. Familial occurrence of nevus sebaceus of jadassohn. Jadassohn nevus article about jadassohn nevus by the. Trichoblastoma is the most common neoplasm developed in nevus sebaceus of jadassohn. Nevus sebaceus of jadassohn definition of nevus sebaceus. The nevus sebaceous of jadassohn in combination with ocular abnormality, convulsions, and mental deficiency constitutes a welldefined though poorly recognized neurocutaneous syndrome. More detailed information about the symptoms, causes, and treatments of nevus sebaceous of jadassohn is available below symptoms of nevus.
Patients should address specific medical concerns with their physicians. Nevus sebaceous of jadassohn is a common skin lesion of children. Most of the time a nevus sebaceus is noticed right at birth, but sometimes it might. T1 familial occurrence of nevus sebaceus of jadassohn. The topic nevus sebaceous of jadassohn you are seeking is a synonym, or alternative name, or is closely related to the medical condition nevus sebaceous. Nevus sebaceus of jadassohn is a congenital abnormality first described by the dermatologist josef jadassohn in 1895. Lesions are usually present at birth and appear as waxy, yelloworange or tan, hairless plaques picture 2c.
N2 we describe two sibs a boy and a girl suffering from linear nevus sebaceus of jadassohn. Such nevi are present at birth, or early childhood, affecting males and females of all races equally. All structured data from the file and property namespaces is available under the creative commons cc0 license. Basal cell carcinoma appearing in a facial nevus sebaceous.
Secondary neoplasms associated with nevus sebaceus of jadassohn. We report the case of a nevus sebaceous of jadassohn in its third stage in a 42yearold male patient. Nevus sebaceous of jadassohn jama pediatrics jama network. A nevus sebaceous is a type of birthmark that usually appears on the scalp. Files are available under licenses specified on their description page. We present a case report of a 30 year old female with a congenital verucous plaque in the scalp localized at the pariental region that had erosion and hematic scabs.
It starts as a flat pink or orange plaque slightly raised area. Multifocal basalcell carcinomas in a nevus sebaceus of. Family practice notebook 2020, family practice notebook, llc. This website is intended for pathologists and laboratory personnel, who understand that medical information is imperfect and must be interpreted using reasonable medical judgment. Twelve cases in the past seven years were encountered in the pediatric practice of one of the authors aec. The nevus sebaceous of jadassohn nsj is a congenital hamartoma that usually affects the face or scalp. It is generally present at birth or in early childhood, but at times it may arise in adult life. Nevus sebaceous is a congenital skin condition which typically appears on the scalp, but may also develop on the face or neck. This type of birthmark is a small area of skin that has too many oil glands that grow larger than normal. Dermoscopy is a noninvasive imaging technique that has proved useful for diagnosing a number of skin lesions through the. Linear nevus sebaceous syndrome lnss is a condition characterized by the association of a large, linear sebaceous nevus type of birthmark with a broad range of abnormalities that may affect every organ system, including the central nervous system cns. Nevus sebaceus of jadassohn how is nevus sebaceus of.
A read is counted each time someone views a publication summary such as the title, abstract, and list of authors, clicks on a figure, or views or downloads the fulltext. It may also appear on the face but this is less common. Nevus sebaceous or sebaceous naevus is a congenital malformation that occurs as a 12 cm plaque. Sebaceous naevus of jadassohn and primary mediastinal.
Skin nonmelanocytic tumor nevus sebaceus of jadassohn. Key points congenital skin condition which typically develops on the scalp, face, or neck. The organoid nevus syndrome is an oculoneurocutaneous condition characterized by the sebaceous nevus of jadassohn, cerebral atrophy, epibulbar complex choristoma, posterior scleral cartilage, and occasionally other features. Nevus sebaceus a nevus sebaceus also known as nevus of jadassohn is an uncommon type of birthmark seen in about 0. The treatment was surgical with seriated excisions and discoloring pulsated laser. The nevus usually is located on the face, scalp, or neck. The monarch initiative brings together data about this condition from humans and other species to help physicians and biomedical researchers.
Dermis nevus sebaceous of jadassohn information on the. A rare genetic neurocutaneous disorder characterized by epidermal nevi associated with central nervous and skeletal system abnormalities. Ths les on is en hamartona with a well circumscribed alopecic plaque shape, whose ciarneter varies frorr less than one to a few cm. It is caused by benign hyperplasia of sebaceous glands. Nevus lipomatosus cutaneus superficialis associated with. The association presented in this third stage case was to a basocelular carcinoma. Sebaceous nevus of jadassohn is a hamartoma that may be associated with malignant or benign tumors. Nevus sebaceus of jadassohn how is nevus sebaceus of jadassohn abbreviated. Josef jadassohn in 1895 first described nevus sebaceus. Caracteristicas clinicas e histopatologicas del nevus.
Even though present at birth, it is more readily seen at 1 month to 6 weeks of age. All content on this website, including dictionary, thesaurus, literature, geography, and other reference data is for informational purposes only. Circumscribed lesion that occurs mainly on the face and scalp and consists predominantly of sebaceous glands, abortive hair follicles and ectopic apocrine glands. A nevus sebaceous is a rare type of birthmark that can be found on the face, neck, forehead, or scalp.
Monarchs tools are designed to make it easier to compare the signs and symptoms phenotypes of different diseases and. Nevus sebaceus of jadassohn, he 40x 4905 nevus sebaceus. Secondary neoplasms associated with nevus sebaceus of. While it can appear anywhere on the head, it most often occurs on the scalp. In the older infant, the growth of hair around the nevus accentuates the lesion.
1508 518 1393 146 1223 1198 1170 187 148 855 223 95 177 183 855 1226 187 1106 294 199 1219 1094 1387 625 1374 1230 1370 1033 250 955 962 509 644